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PAH


Official Full Name
phenylalanine hydroxylase
Organism
Homo sapiens
Gene ID
5053
Background
This gene encodes a member of the biopterin-dependent aromatic amino acid hydroxylase protein family. The encoded phenylalanine hydroxylase enzyme hydroxylates phenylalanine to tyrosine and is the rate-limiting step in phenylalanine catabolism. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria. [provided by RefSeq, Aug 2017]
Synonyms
PH; PKU; PKU1

Cat.No. Product Name Price
SHH370080 shRNA set against Mouse PAH (NM_008777.3) Inquiry
SHH370084 shRNA set against Rat PAH (NM_012619.2) Inquiry
SHR078414 shRNA set against Human PAH(NM_000277.1) Inquiry
SHW000025 shRNA set against Chicken PAH (NM_001001298) Inquiry
SHW016720 shRNA set against Danio rerio PAH (NM_200551) Inquiry
Cat.No. Product Name Price
CDFH013622 Human PAH cDNA Clone(NM_000277.1) Inquiry
CDFR010438 Rat Pah cDNA Clone(NM_012619.2) Inquiry
MiUTR1H-07472 PAH miRNA 3'UTR clone Inquiry
MiUTR1R-05604 PAH miRNA 3'UTR clone Inquiry
CDCB161500 Chicken PAH ORF Clone (NM_001001298) Inquiry
CDCB178195 Danio rerio PAH ORF Clone (NM_200551) Inquiry
CDCB185129 Rabbit PAH ORF clone (XM_002711296.2) Inquiry
CDCH016580 Mouse PAH ORF clone(NM_008777.3) Inquiry
CDCL185598 Human PAH ORF clone(NM_000277.1) Inquiry
CDCR377485 Rat Pah ORF Clone(NM_012619.2) Inquiry
CDCS405543 Human PAH ORF Clone (BC026251) Inquiry
Cat.No. Product Name Price
CC-1008 PAH Easy KO Kit Inquiry
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