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PEX7


Official Full Name
peroxisomal biogenesis factor 7
Organism
Homo sapiens
Gene ID
5191
Background
This gene encodes the cytosolic receptor for the set of peroxisomal matrix enzymes targeted to the organelle by the peroxisome targeting signal 2 (PTS2). Defects in this gene cause peroxisome biogenesis disorders (PBDs), which are characterized by multiple defects in peroxisome function. There are at least 14 complementation groups for PBDs, with more than one phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene have been associated with PBD complementation group 11 (PBD-CG11) disorders, rhizomelic chondrodysplasia punctata type 1 (RCDP1), and Refsum disease (RD). [provided by RefSeq, Oct 2008]
Synonyms
RD; PBD9B; PTS2R; RCDP1

Cat.No. Product Name Price
SHH373816 shRNA set against Human PEX7 (NM_000288.3) Inquiry
SHH373820 shRNA set against Mouse PEX7 (NM_008822.2) Inquiry
SHH373824 shRNA set against Rat PEX7 (NM_001034147.1) Inquiry
SHR103876 shRNA set against Rat Pex7(NM_001034147.1) Inquiry
SHW004025 shRNA set against Chicken PEX7 (NM_001277709) Inquiry
SHW008085 shRNA set against Danio rerio PEX7 (NM_001013532) Inquiry
Cat.No. Product Name Price
CDCS405551 Human PEX7 ORF Clone (BC006268) Inquiry
CDFR004378 Rat Pex7 cDNA Clone(NM_001034147.1) Inquiry
MiUTR1R-05773 PEX7 miRNA 3'UTR clone Inquiry
MiUTR3H-04388 PEX7 miRNA 3'UTR clone Inquiry
SKO0667 PEX7 Validated sgRNA vector Inquiry
CDCB158102 Human PEX7 ORF clone (BC006268) Inquiry
CDCB165500 Chicken PEX7 ORF Clone (NM_001277709) Inquiry
CDCB169560 Danio rerio PEX7 ORF Clone (NM_001013532) Inquiry
CDCB193173 Rabbit PEX7 ORF clone (XM_002714756.2) Inquiry
CDCL148231 Mouse Pex7 ORF clone (NM_001161825.1) Inquiry
CDCR245723 Mouse Pex7 ORF Clone(NM_008822.2) Inquiry
CDCR371406 Rat Pex7 ORF Clone(NM_001034147.1) Inquiry
CDCS405550 Human PEX7 ORF Clone (BC031606) Inquiry
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