Official Full Name
prenyl (decaprenyl) diphosphate synthase, subunit 2
The protein encoded by this gene is an enzyme that synthesizes the prenyl side-chain of coenzyme Q, or ubiquinone, one of the key elements in the respiratory chain. The gene product catalyzes the formation of all trans-polyprenyl pyrophosphates from isopentyl diphosphate in the assembly of polyisoprenoid side chains, the first step in coenzyme Q biosynthesis. Defects in this gene are a cause of coenzyme Q10 deficiency.
PDSS2; prenyl (decaprenyl) diphosphate synthase, subunit 2; C6orf210, chromosome 6 open reading frame 210; decaprenyl-diphosphate synthase subunit 2; bA59I9.3; C6orf210; Candidate tumor suppressor protein; chromosome 6 open reading frame 210; decaprenyl pyrophosphate synthetase subunit 2; DLP1; hDLP1; subunit 2 of decaprenyl diphosphate synthase; decaprenyl pyrophosphate synthase subunit 2; all-trans-decaprenyl-diphosphate synthase subunit 2; zgc:92156