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PEX5


Official Full Name
peroxisomal biogenesis factor 5
Organism
Homo sapiens
Gene ID
5830
Background
The product of this gene binds to the C-terminal PTS1-type tripeptide peroxisomal targeting signal (SKL-type) and plays an essential role in peroxisomal protein import. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of neonatal adrenoleukodystrophy (NALD), a cause of Zellweger syndrome (ZWS) as well as may be a cause of infantile Refsum disease (IRD). Alternatively spliced transcript variants encoding different isoforms have been identified. [provided by RefSeq, Oct 2008]
Synonyms
PXR1; PBD2A; PBD2B; PTS1R; RCDP5; PTS1-BP

Cat.No. Product Name Price
SHR104074 shRNA set against Mouse Pex5(NM_008995.2) Inquiry
SHW000986 shRNA set against Chicken PEX5 (NM_001012818) Inquiry
SHH373780 shRNA set against Human PEX5 (NM_000319.4) Inquiry
SHH373784 shRNA set against Mouse PEX5 (NM_175933.2) Inquiry
SHR103872 shRNA set against Mouse Pex5(NM_175933.2) Inquiry
SHR104098 shRNA set against Mouse Pex5(NM_175933.2) Inquiry
SHW017261 shRNA set against Danio rerio PEX5 (NM_201156) Inquiry
Cat.No. Product Name Price
CDFH014100 Human PEX5 cDNA Clone(NM_001131023.1) Inquiry
MiUTR3H-03359 PEX5 miRNA 3'UTR clone Inquiry
MiUTR3H-03358 PEX5 miRNA 3'UTR clone Inquiry
MiUTR3H-03357 PEX5 miRNA 3'UTR clone Inquiry
MiUTR3H-03356 PEX5 miRNA 3'UTR clone Inquiry
MiUTR1M-09124 PEX5 miRNA 3'UTR clone Inquiry
MiUTR1M-09123 PEX5 miRNA 3'UTR clone Inquiry
CDFL010161 Mouse Pex5 cDNA Clone(NM_175933.2) Inquiry
CDFH014103 Human PEX5 cDNA Clone(NM_001131026.1) Inquiry
CDFH014102 Human PEX5 cDNA Clone(NM_001131025.1) Inquiry
CDFH014101 Human PEX5 cDNA Clone(NM_001131024.1) Inquiry
MiUTR3H-03360 PEX5 miRNA 3'UTR clone Inquiry
SKO1097 PEX5 Validated sgRNA vector Inquiry
CDCL148188 Human PEX5 ORF clone (NM_001131023.1) Inquiry
CDCR349834 Human PEX5 ORF Clone(NM_001131026.1) Inquiry
CDCR246520 Mouse Pex5 ORF Clone(NM_008995.2) Inquiry
CDCL148195 Mouse Pex5 ORF clone (NM_175933.2) Inquiry
CDCL148191 Human PEX5 ORF clone (NM_001131025.1) Inquiry
CDCL148189 Human PEX5 ORF clone (NM_001131024.1) Inquiry
CDCG000298 Rat PEX5 ORF clone(NM_001170584.1) Inquiry
CDCB191587 Rabbit PEX5 ORF clone (XM_008259775.1) Inquiry
CDCB178736 Danio rerio PEX5 ORF Clone (NM_201156) Inquiry
CDCB162461 Chicken PEX5 ORF Clone (NM_001012818) Inquiry
CDCS405580 Human PEX5 ORF Clone (BC010621) Inquiry
CDCB158446 Human PEX5 ORF clone (BC010621) Inquiry
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